Dermatofibrosarcoma Protuberans - Delayed diagnosis in a Young Male
DOI:
https://doi.org/10.51985/JBUMDC2025531Keywords:
CD34 Antigen, Dermatofibrosarcoma Protuberans, Soft Tissue Neoplasms, Local Excision, Surgical MeshAbstract
The dermatofibrosarcoma Protuberans is a cutaneous tumor that grows slowly. It is commonly misdiagnosed as other common abdominal swellings, such as fibromas or lipomas. Recurrence is frequently seen. A male patient, 27, presented with a complaint of Right iliac fossa (RIF) swelling that had persisted for 17 years. A lumpectomy was performed on the patient because of its growing size. Histopathology verified the presence of Dermatofibrosarcoma Protuberans (DFSP). A Wide Local Excision (WLE) with mesh repair was performed, biopsy revealed elongated monomorphic spindle cells that extended in a storiform pattern into the deeper subcutaneous fat with negative margins. Immunohistochemistry verified that it was DFSP. A 17-year diagnosis delay is highlighted in the current report. Delays are further exacerbated by the asymptomatic nature and lack of knowledge among community physicians. For any chronic, asymptomatic, indolent parietal wall swelling, local physicians should take DFSP into consideration as a differential diagnosis
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