Kartagener’s Syndrome Presenting As Bilateral Recurrent Nasal Polyposis In A Young Boy
DOI:
https://doi.org/10.51985/JBUMDC2018076Keywords:
sinusitis, primary ciliary dyskinesia, Kartagener's syndrome, situs inversus BronchiectasisAbstract
Kartagener's syndrome is a very rare congenital disease consists of a classic triad, sinusitis, situs inversus and bronchiectasis.
Approximately one half of patients with primary ciliary dyskinesia have situs inversus and Kartagener syndrome. We are
presenting a case of Kartagener’s syndrome in a 10-year-old boy presented with chronic sinusitis leading to bilateral multiple
nasal polyposis. He also had situs inversus and chronic bronchiectasis. He had undergone surgery two years back for nasal
polyposis but now again presenting as recurrent nasal polyposis. In order to prevent the dreadful complications correct
diagnosis in early life is very important in such patients.
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Copyright (c) 2018 Zeba Ahmed; Warda Waseem, Uroosa Saman
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